Internal jugular vein (LJV) phlebectasia is a rare form of congenital venous anomaly. Less than 50 cases have been reported in the literature world-wide. In the majority of cases the lesion was in boys and on the right side. It is a fusiform dilation of the vein without any apparent obstruction, and is believed to be due to congenital thinning of the vessel wall. It can mimic an external laryngocele.